Perioral pigmentation: what is your diagnosis?
نویسندگان
چکیده
Pigmented spots in the skin and mucosa (lentigines) can be found in various diseases called familial lentiginosis syndromes; Peutz-Jeghers syndrome (PJS) is one of them. It is characterized by the association of mucocutaneous melanin pigmentation and hamartomatous gastrointestinal polyps. Patients with PJS are at increased risk of intussusception and cancer development (gastrointestinal and non-gastrointestinal tumors). We present a 5-year-old girl with pigmented macules of perioral and perinasal skin, lips, and buccal mucosa and review lentiginoses and the surveillance of PJS.
منابع مشابه
A middle-aged lady with an asymptomatic, hyperpigmented plaque on the thigh: what is your diagnosis?
CLINICAL PRESENTATIONA 44-year-old lady came to a dermatology clinic due to an asymptomatic, hyperpigmented plaque on her right thigh since 4 months ago. On physical exam, hypertrichosis on the lesion was notable (Figure 1). Rubbing the lesion resulted in erythema and edema of the lesion. She had no systemic disease and her family history was unremarkable.
متن کاملAn unusual palmoplantar pigmentation.
A 60 year old man had asymptomatic progressive pigmentation of the palms (fig 1), fingertips (fig 2), and soles for the last 20 years. Besides this, he had discoloration of his sclerae (fig 3). He was well but for low backache and joint pains of a few months’ duration. Histopathological examination of the skin lesion was diagnostic (fig 4). Questions (1) What is your diagnosis? (2) What are the...
متن کاملA middle-aged lady with bilateral and symmetrical erythematous patches on her lower extremities: What is your diagnosis?
CLINICAL PRESENTATION A 35-year-old woman presented to the dermatological clinic of Shahid-Faghihi Hospital with asymptomatic, bilateral and symmetrical erythematous patches on her lower extremities. On clinical examination, there were erythematous patches on the lateral and medial malleolar surfaces and superior to the medial malleolus, with no other complaints regarding pain or itching (Figur...
متن کاملQuiz : A middle aged lady with annular athrophic papules and plaques on her back: What is your diagnosis?
A 51 year old woman was referred to dermatology clinic with multiple asymptomatic erythematus papules and plaques on her back, which she had developed over the previous 2 months ago. In the dermatological examination, there were multiple atrophic papules with hypopigmented centers and sharp borders on her back, some of which were annular with elevated violaceous borders (Figures 1, 2). Fu...
متن کاملA teenage girl with bilateral hyperpigmentation of cheeks and sclera and a vascular stain on her cheek: What is your diagnosis?
CLINICAL PRESENTATION A 16 year old girl was referred to dermatology clinic with bilateral blue gray hyperpigmented patches on her cheeks since birth. Upon close physical examination, scleral blue-gray hyperpigmentation was observed in both her eyes (Figure 1). She also had a blanchable red patch with poorly defined borders on her right cheek (Figure 2). Ophthalmology consultation further revea...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- Dermatology online journal
دوره 14 11 شماره
صفحات -
تاریخ انتشار 2008